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X-linked Myotubular Myopathy
  • Description
  • Signalment
  • Clinical Features
  • Neurolocalization
  • Genetics
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X-linked myotubular myopathy is a form of centronuclear myopathy caused by a mutation in the myotubularin (MTM1) gene.
Age of Onset: First few weeks of life
Sex Predisposition: Males are almost exclusively affected
Clinical Course:
​Clinical signs worsen over time
Clinical Signs:
Posture and Appearance
Small stature
Cervical ventroflexion

Movement
Tetraparesis
Ataxia
Difficulty rising
Exercise-intolerance

Cranial Nerves
Dropped jaw
Dysphagia

Spinal Reflexes
Hyporeflexia

Muscle Atrophy
Diffuse muscle atrophy
Diffuse neuromuscular
X-linked mutation in the myotubularin (MTM1) gene

For breed specific genetic testing, follow the links below:

https://labgenvet.ca/en/disease/myotubular-myopathy/
https://www.combibreed.com/myotubular-myopathy-boykin-spaniel/
To read more about this disease click below:
References
Picture
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